Clinical case of Kasabach–Merritt syndrome in the practice of a neonatologist
AbstractKasabach–Merritt syndrome (KMS) is a rare disease characterized by the presence of a vascular tumor with progressive invasive growth, development of thrombocytopenia and consumptive coagulopathy. In the neonatal period, the disease can characterized by the skin manifestations and hide under the guise of an intrauterine infection. Depending on the location in different organs and systems, multiple organ failure develops. The article discusses modern approaches of the management of patients with KMS, and also given the description in a clinical case of the newborn with KMS. Manifestations of this syndrome were noted from birth. The presence of concomitant pathology can cause difficulties in making a right way of diseases.
Keywords:newborn; hemangioma; thrombocytopenia; consumption coagulopathy
Funding. The study had no sponsor support.
Conflict of interest. The authors declare no conflict of interest.
Contribution. Research concept – Shumilov P.V.; general management – Levchenko L.A., Sarkisyan H.A.; collection of biomaterial and information – Shishkina V.V., Chuyko Ya.M., Markov S.E.
For citation: Levchenko L.A., Shumilov P.V., Sarkisyan H.A., Shishkina V.V., Chuyko Ya.M., Markov S.E. Clinical case of Kasabach–Merritt syndrome in the practice of a neonatologist. Neonatologiya: novosti, mneniya, obuchenie [Neonatology: News, Opinions, Training]. 2023; 11 (4): 26–35. DOI: https://doi.org/10.33029/2308-2402-2023-11-4-26-35 (in Russian)
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