Interstitial diseases of developing lungs

• Dmitry Yu. Ovsyannikov
• Boytsova E.V.
• Maxim A. Karpenko
• Maria A. Zhestkova
• Elena V. Makarenko
• Alexeeva Olga V.
• Valeria A. Strelnikova
• Igor S. Davydov

Abstract

The review is based on the literature data and the results of the own research. It provides information on the main interstitial diseases of developing lungs, representing a separate group of interstitial lung diseases specific for newborns and infants. Diffuse disorders of lung development, pulmonary hypoplasia, neuroendocrine cellular hyperplasia of infants, pulmonary interstitial glycogenosis, and chronic pneumonitis of infants are considered. Information on the possible etiology, pathomorphology, clinical diagnosis, CT semiotics, and therapy of these rare diseases were consistently presented.

Keywords:interstitial lung diseases; children; diffuse lung development disorders; pulmonary hypoplasia; neuroendocrine cellular hyperplasia of infants; pulmonary interstitial glycogenosis; chronic pneumonitis of infants

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